Background. When choosing the optimal type of surgical correction in patients with congenital heart defects (CHD), it is necessary to focus on a comprehensive echocardiographic study (Echo-CG). Coarctation of the aorta is a complex congenital heart disease in terms of diagnostics, therefore, it is important to use three-dimensional echo-CG in its diagnosis.
Description of the clinical case. In the presented clinical case, congenital heart disease (aortic arch hypoplasia) was detected in the fetus at the 19th week of gestation. An examination and long-term follow-up of a pregnant woman at the Cardiac Surgery Center in Astrakhan confirmed the diagnosis.
Results. Immediately after birth, the child underwent surgical treatment of a heart defect. Subsequently, during dynamic follow-up of the patient in the early and late stages of the postoperative period, no serious complications were identified.
Conclusion. Thus, accurate early antenatal diagnosis made it possible to determine the optimal routing of the child after birth and to pre-select tactics for timely correction of congenital heart disease, which ensured a favorable course of the postoperative period. This proves the great importance of prenatal diagnosis of critical heart defects using echocardiography.

Keywords: hypoplasia of the aortic isthmus, cardiac surgical correction, aortic arch obstruction, antenatal diagnosis, fetus, coarctation of the aorta, echocardiography